Respiratory Trials·org

Cystic fibrosis · CFTR modulators

SKYLINE

Vanzacaftor-tezacaftor-deutivacaftor versus elexacaftor-tezacaftor-ivacaftor

SKYLINE trial design and results
Design Two randomised, double-blind, active-controlled, non-inferiority trials
Treatment Once-daily vanzacaftor with tezacaftor and deutivacaftor
Control Twice-daily elexacaftor with tezacaftor and ivacaftor
Population 398 participants in trial VX20-121-102 and a larger cohort in VX20-121-103; median age 31 years
Follow-up 52 weeks
Primary endpoint Non-inferiority for absolute change in percentage predicted FEV1
Result Vanzacaftor-tezacaftor-deutivacaftor was non-inferior to elexacaftor-tezacaftor-ivacaftor for percentage predicted FEV1, and was safe and well tolerated.
Secondary endpoints Sweat chloride, CFQ-R respiratory domain, safety

Vanzacaftor-tezacaftor-deutivacaftor is non-inferior to elexacaftor-tezacaftor-ivacaftor in terms of FEV1 % predicted, and is safe and well tolerated. Once daily dosing with vanzacaftor-tezacaftor-deutivacaftor reduces treatment burden, potentially improving adherence, compared with the twice daily regimen of the current standard of care.

The trial authors, in the published abstract

How it has aged

Not a step up in efficacy but in convenience — the argument is adherence and treatment burden, which in a lifelong therapy is not a trivial one. Whether it displaces VX17-445-102 will turn on CFTR restoration and the range of variants covered rather than on FEV1.

Publications

Vanzacaftor-tezacaftor-deutivacaftor versus elexacaftor-tezacaftor-ivacaftor in individuals with cystic fibrosis aged 12 years and older (SKYLINE Trials VX20-121-102 and VX20-121-103): results from two randomised, active-controlled, phase 3 trials

Keating C, Yonker LM, Vermeulen F, et al. Vanzacaftor-tezacaftor-deutivacaftor versus elexacaftor-tezacaftor-ivacaftor in individuals with cystic fibrosis aged 12 years and older (SKYLINE Trials VX20-121-102 and VX20-121-103): results from two randomised, active-controlled, phase 3 trials. Lancet Respir Med 2025 Mar;13(3):256-271.

  • Non-inferior to elexacaftor-tezacaftor-ivacaftor for percentage predicted FEV1
  • Once-daily rather than twice-daily dosing
  • Safety and tolerability comparable